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  • Convegno ASBBI 23 settembre 2023
Testo del convegno 

Presentazione 

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Curriculum vitae


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Pubblicazioni:

Metabolomic fingerprinting of renal disease progression in Bardet-Biedl syndrome reveals mitochondrial dysfunction in kidney tubular cells.                                                                                             
Salvatore Tolone;Ludovico Docimo;Valentina Di Iorio;Francesca Simonelli;Alessandra Perna;Vincenzo Nigro; Giovambattista Capasso Miriam Zacchia   -  2022
https://pubmed.ncbi.nlm.nih.gov/36281451/
                                                                                                                                                                           
Macular abnormalities in Italian patients with retinitis pigmentosa.                                                     
Francesco Testa, Settimio Rossi, Raffaella Colucci, Beatrice Gallo, Valentina Di Iorio, Michele della Corte, Claudio Azzolini, Paolo Melillo, Francesca Simonelli
https://pubmed.ncbi.nlm.nih.gov/24532797/

The renal lesions in Bardet-Biedl Syndrome: history before and after the discovery of BBS genes: 
Zacchia Miriam; Simonelli Francesca; Di Iorio Valentina;Anastasio Pietro;Capasso Giovambattista  - 2018
https://pubmed.ncbi.nlm.nih.gov/29482283/

Patho-physiology of renal dysfunction in Bardet-Biedl Syndrome                                                                                                          
Zacchia M;  Di Iorio Valentina; Capolongo G;Rinaldi L; Capasso G.                                        
https://europepmc.org/article/med/28963828
                                                                                                                                                                                                                    
Genetic characterization of Italian patients with Bardet-Biedl syndrome and correlation to ocular, renal and audio-vestibular phenotype: Identification of eleven novel pathogenic sequence variants
ESPOSITO, GABRIELLA;TESTA, Francesco;ZACCHIA, Miriam;Di Iorio, Valentina;Capolongo, Giovanna;Rinaldi, Luca;ROSSI, Settimio;CAPASSO, Giovambattista;SIMONELLI, Francesca;
https://pubmed.ncbi.nlm.nih.gov/28143435/ 

Mutations in the PCYT1A gene are responsible for isolated forms of retinal dystrophy.
Testa F, Filippelli M, Brunetti-Pierri R, Di Fruscio G, Di Iorio V, Pizzo M, Torella A, Barillari MR, Nigro V, Brunetti-Pierri N, Simonelli F, Banfi S.
 https://iris.unicampania.it/handle/11591/371060
 
 
Clinical and Genetic Evaluation of a Cohort of Pediatric Patients with Severe Inherited Retinal Dystrophies.
Di Iorio V, Karali M, Brunetti-Pierri R, Filippelli M, Di Fruscio G, Pizzo M, Mutarelli M, Nigro V, Testa F, Banfi S, Simonelli F.
https://pubmed.ncbi.nlm.nih.gov/29053603/
 

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